WOAH reported bovine spongiform encephalopathy (BSE) prion, atypical strain, H-type in Cornwall, England, in a 17 year-old indigenous cow on a beef suckler farm, detected during routine national TSE statutory surveillance and testing of fallen stock cattle aged over 48 months. The animal was not presented for slaughter and did not enter the food chain, there is no threat to food safety or human health. The detection of this isolated, single case of atypical BSE does not change the UK’s BSE disease risk status.